Perspective validation of the eurofever classification criteria for monogenic periodic fevers
- Autori: Federici S; Dolezalova P; Cantarini L; Papadopoulou-Alataki E; Alessio M; Herlin T; Gueli I; Modesto C; Fabio G; Maggio MC; Rua Elorduy MJ, Garibotto F; Insalaco A; Kozlova A; Anton J; Brik R; Frenkel J; Hoppenreijs E; Sormani MP; Martini A; Gattorno M
- Anno di pubblicazione: 2014
- Tipologia: eedings
- OA Link: http://hdl.handle.net/10447/98616
Abstract
We recently proposed a set of provisional, evidence-based, clinical criteria for the classification of children and adults patients affected by monogenic periodic fevers. These criteria, built and validated in a cohort of 1215 patients with periodic fever enrolled in the Eurofever Registry from November 2009 to February 2013, displayed a high sensitivity and specificity.